Prions are the causal agent in Mad Cow disease, Scrapies (in sheep), Chronic Wasting disease in deer and elk and a form of Creutzfeldt-Jakob disease in humans.
|Source Michigan is running about 1.5 diagnosed cases of CJ disease per million per year.|
Prions are incredibly durable, presumably due to their simple structure. Mad Cow disease in Britain became an issue because the normal cooking procedures for recycling slaughtered animal wastes back into animal food did not kill the prions that were in the central nervous system.
|States reporting Chronic Wasting Disease|
Loss of the ability to export beef and dairy products would have a devastating effect on the already teetering farm economy.